HC Deb 30 January 2003 vol 398 cc1011-3W
Mrs. Spelman

To ask the Secretary of State for Health (1) what the incidence of osteoglophonic dysplasia per thousand live births was(a) nationally, (b) in Solihull and (c) in the south of Solihull in each of the last three decades; [93856]

(2) how many cases of osteoglophonic dysplasia were recorded (a) in the United Kingdom, (b) in Solihull and (c) in the south of Solihull in each of the last three decades. [93855]

Ruth Kelly

I have been asked to reply.

The information requested falls within the responsibility of the National Statistician. I have asked him to reply.

Letter from L. Cook to Mrs. Caroline Spelman, dated 30 January 2003: As National Statistician, I have been asked to reply to your recent questions asking for the incidence number and rate for osteoglophonic dysplasia reported nationally, in Solihull and in the south of Solihull in each of the last three decades. (93855, 93856) The National Congenital Anomaly System (NCAS), based at the Office for National Statistics (ONS), codes all anomalies using the International Classification of Diseases (ICD). Between 1968 and 1988, using the 8th and 9th revisions of ICD, osteoglophonic dysplasia was assigned to a code that also included a number of other anomalies of the skull and face bones. Therefore it is not possible to identify number of babies born with osteoglophonic dysplasia prior to 1988. However from 1989, notifications held on NCAS contained descriptive text of the anomalies present. It is therefore possible to identify cases of osteoglophonic dysplasia from 1989. With the introduction of the 10th revision of ICD in 1995, osteoglophonic dysplasia has been separately coded. Prior to 1995, ONS collected all notifications of congenital anomalies that were identified within ten days of birth. From 1995, ONS has collected all notifications of congenital anomalies whenever they are identified. The attached table shows the number of babies in England and Wales notified to the National Congenital Anomaly System with osteoglophonic dysplasia and rate per 10,000 live births for the years 1989 to 2001. During this period there was only one case of osteoglophonic dysplasia reported to the NCAS in Solihull health authority in 1994. Figures from NCAS are not routinely published below health authority level.

Live born babies notified to the National Congenital Anomaly
System with osteoglophonic dysplasia1. England and Wales,
numbers and rates per 10000 live births
Numbers Rate per 10000 live births
1989 2 0.03
1990 3 0.04
1991 1 0.01
1992 2 0.03
1993 0
1994 0

Live born babies notified to the National Congenital Anomaly
System with osteoglophonic dysplasia1. England and Wales,
numbers and rates per 10000 live births
Numbers Rate per 10000 live births
1995 2 0.03
1996 1 0.02
1997 1 0.02
1998 7 0.03
1999 0
2000 1 0.02
2001 0
1During 1989–1994, under the 9th revision of the International Classification of Diseases, cases coded as 756.0 were searched for the term osteoglophonic dysplasia or its synonyms craniofacial dysostosis and Crouzon's disease.

During 1995–2001, under the 10th revision of the International Classification of Diseases, any cases with code Q75.1 were selected.

Source:

National Congenital Anomaly System @ 28 January 2003

Mrs. Spelman

To ask the Secretary of State for Health (1) what the incidence of severe hypoplastic left heart syndrome per thousand live births was(a) in the United Kingdom, (b) in Solihull and (c) in the south of Solihull in each of the last three decades; [93854]

(2) how many cases of severe hypoplastic left heart syndrome were recorded (a) in the United Kingdom, (b) in Solihull and (c) in the south of Solihull in each of the last three decades. [93853]

Ruth Kelly

I have been asked to reply.

The information requested falls within the responsibility of the National Statistician. I have asked him to reply.

Letter from L. Cook to Mrs. Caroline Spelman, dated 30 January 2003: As National Statistician, I have been asked to reply to your recent questions asking for the incidence number and rate (per thousand live births) of severe hypoplastic left heart syndrome reported nationally, in Solihull and in the south of Solihull in each of the last three decades. (93854, 93853) The National Congenital Anomaly System (NCAS), based at Office for National Statistics (ONS), codes all anomalies using the International Classification of Diseases (ICD). Between 1968 and 1978, when the 8th revision of ICD was used, hypoplastic left heart syndrome was assigned to a code that also includes a number of other specific anomalies of the heart. Therefore it is not possible to identify number of babies born with hypoplastic left heart syndrome prior to 1979. Since the introduction of the 9th revision of ICD in 1979, hypoplastic left heart syndrome has been separately coded. It is therefore possible to provide the information requested from 1979 onwards. Prior to 1995, ONS collected all notifications of congenital anomalies that were identified within ten days of birth. From 1995, ONS has collected all notifications of congenital anomalies whenever they are identified. The attached table shows the number of babies in England and Wales notified to the National Congenital Anomaly System with hypoplastic left heart syndrome and rate per 1,000 live births for the years 1979 to 2001. During this period there was only one case of hypoplastic left heart syndrome reported to NCAS in Solihull health authority in 1999. Figures from NCAS are not routinely published below health authority level.

Live born babies notified to the National Congenital Anomaly
System with hypoplastic left heart syndrome1, England and Wales,
numbers and rates per 1000 live births
Numbers Rate per 1000 live births
1979 6 0.01
1980 10 0.02
1981 8 0.01
1982 13 0.02
1983 18 0.03
1984 20 0.03
1985 24 0.04
1986 16 0.02
1987 18 0.03
1988 9 0.01
1989 24 0.03
1990 13 0.02
1991 10 0.01
1992 13 0.02
1993 8 0.01
1994 26 0.04
1995 16 0.02
1996 28 0.04
1997 32 0.05
1998 18 0.03
1999 33 0.05
2000 39 0.06
2001 33 0.06
1Hypoplastic left heart syndrome is coded as:

1979–199 9th revision of the International Classification of Diseases—code 746.7

1995–200 10th revision of the International Classification of Diseases—code Q23.4

Source:

National Congenital Anomaly System @ 28 January 2003